Hemochromatosis ke eng

Hemochromatosis ke eng

Hemochromatosis (eo hape e bitsoang genetic hemochromatosis kapa hereditary hemochromatosis) ke lefu la lefutso le lefutso le ikarabellang bakeng sa lefu lena. ho monya tshepe ka tsela e feteletseng ka mala le a ona bokella mmeleng.

Lisosa tsa hemochromatosis

Hemochromatosis ke lefu la liphatsa tsa lefutso le amanang le a phetoho ya lefutso le le leng kapa ho feta. Liphetoho tsena li bonoa libakeng tse fapaneng tsa lefats'e 'me e' ngoe le e 'ngoe e lumellana le polelo e tebileng ea lefu lena.

THEhemochromatosis HFE ea lefutso (hape e bitsoa mofuta oa I hemochromatosis) ke mofuta o atileng haholo oa lefu lena. E hokahane le phetoho ea mofuta oa HFE e fumanehang ho chromosome 6.

Khafetsa ea lefu lena

Hemochromatosis ke e 'ngoe ea mafu a atileng haholo a lefutso.

Hoo e ka bang motho a le mong ho ba 1 o na le bothata ba liphatsa tsa lefutso bo etsang hore lefu lena le qale1. Empa se tlamehang ho utloisisoa hona joale ke hore lefu lena le ka ba le pontšo ea kliniki ea matla a feto-fetohang e le hore mefuta e matla ea hemochromatosis e lule e le seoelo.

Batho ba anngoeng ke lefu lena

The banna ba ameha hangata ho feta basali (banna ba 3 bakeng sa mosali a le mong).

Matšoao a hlaha hangata Lilemo tse 40 kamora moo empa e ka qala pakeng tsa lilemo tse 5 le 30 (juvenile hemochromatosis).

Lefu lena le bonoa khafetsa libakeng tse ling tsa lefats'e, mohlala, United States kapa Europe leboea. Ha e fumanehe linaheng tsa Asia Boroa-bochabela kapa ho batho ba batšo.

Fora, libaka tse ling (Brittany) li ameha haholo.

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